Title : Intracranial Extramedullary Hematopoiesis as “Ghost Tumor (Meningioma)”: First Case Report in Sickle Cell Disease and Review of Literature
Abstract:
Extramedullay hematopoiesis (EMH) is a common compensatory phenomenon to chronic hemolytic anemias. Commonly occurs in the liver, spleen, kidney, lymph nodes and also been reported in skin, adrenal gland, thymus, ovary, paraspinal regions of thorax, pelvic region and the process can often manifest as a mass or mimicking neoplasm. An Intracranial EMH is an extremely rare occurrence and has been more commonly reported in patients with Thalassemia, Myelofibrosis and we did not come across a report in Sickle Cell disease. We are reporting a 26 year-old male with sickle cell disease, who present with generalized seizure and was diagnosed elsewhere to have a left sphenoid wing meningioma and was offered surgery but he refuse at that time. One year later, patient presented to our ER with generalized seizure and wants to go for surgery. His repeat MRI Brain revealed no lesion suggesting complete spontaneous resolution previously noted lesion (tumor). We present this case and review the related literature
What will audience learn from your presentation?
- Don’t rush to do a final diagnosis without full work up and an opinion of your senior colleagues
- Rare and unusual cases needs to be investigated individually and in multidisciplinary panel
- If its rare case, then reporting it is a good idea.
